Summary: international consensus statement on nomenclature and classification of the congenital bicuspid aortic valve and its aortopathy, for clinical, surgical, interventional and research purposes

Michelena, H.I.; Corte, A. della; Evangelista, A.; Maleszewski, J.J.; Edwards, W.D.; Roman, M.J.; ... ; Schafers, H.J. (2021)

Article / Letter to editor

This International evidence-based nomenclature and classification consensus on the congenital bicuspid aortic valve and its aortopathy recognizes 3 types of bicuspid aortic valve: 1. Fused type, with 3 phenotypes: right-left cusp fusion, right-non cusp fusion and left-non cusp fusion; 2. 2-sinus type with 2 phenotypes: Latero-lateral and antero-posterior; and 3. Partial-fusion or forme fruste. This consensus recognizes 3 bicuspid-aortopathy types: 1. Ascending phenotype; root phenotype; and 3. extended phenotypes.

• Bicuspid aortic valve
• Aortopathy
• Nomenclature
• Classification

• All authors: Michelena, H.I.; Corte, A. della; Evangelista, A.; Maleszewski, J.J.; Edwards, W.D.; Roman, M.J.; Devereux, R.B.; Fernandez, B.; Asch, F.M.; Barker, A.J.; Sierra-Galan, L.M.; Kerchove, L. de; Fernandes, S.M.; Fedak, P.W.M.; Girdauskas, E.; Delgado, V.; Abbara, S.; Lansac, E.; Prakash, S.K.; Bissell, M.M.; Popescu, B.A.; Hope, M.D.; Sitges, M.; Thourani, V.H.; Pibarot, P.; Chandrasekaran, K.; Lancellotti, P.; Borger, M.A.; Forrest, J.K.; Webb, J.; Milewicz, D.M.; Makkar, R.; Leon, M.B.; Sanders, S.P.; Markl, M.; Ferrari, V.A.; Roberts, W.C.; Song, J.K.; Blanke, P.; White, C.S.; Siu, S.; Svensson, L.G.; Braverman, A.C.; Bavaria, J.; Sundt, T.M.; Khoury, G. el; Paulis, R. de; Enriquez-Sarano, M.; Bax, J.J.; Otto, C.M.; Schafers, H.J.
• Date: 2021-09-01
• Journal: European Journal of Cardio-Thoracic Surgery
• Volume: 60
• Issue: 3
• Pages: 481 - 496
• DOI: doi:10.1093/ejcts/ezab039