International consensus statement on nomenclature and classification of the congenital bicuspid aortic valve and its aortopathy, for clinical, surgical, interventional and research purposes

Michelena, H.I.; Corte, A. della; Evangelista, A.; Maleszewski, J.J.; Edwards, W.D.; Roman, M.J.; ... ; Int Bicuspid Aortic Valve Consorti (2021)

Article / Letter to editor

This International Consensus Classification and Nomenclature for the congenital bicuspid aortic valve condition recognizes 3 types of bicuspid valves: 1. The fused type (right-left cusp fusion, right-non-coronary cusp fusion and left-non-coronary cusp fusion phenotypes); 2. The 2-sinus type (latero-lateral and antero-posterior phenotypes); and 3. The partial-fusion (forme fruste) type. The presence of raphe and the symmetry of the fused type phenotypes are critical aspects to describe. The International Consensus also recognizes 3 types of bicuspid valve-associated aortopathy: 1. The ascending phenotype; 2. The root phenotype; and 3. Extended phenotypes.

• Bicuspid aortic valve
• Aortopathy
• Nomenclature
• Classification

• All authors: Michelena, H.I.; Corte, A. della; Evangelista, A.; Maleszewski, J.J.; Edwards, W.D.; Roman, M.J.; Devereux, R.B.; Fernandez, B.; Asch, F.M.; Barker, A.J.; Sierra-Galan, L.M.; Kerchove, L. de; Fernandes, S.M.; Fedak, P.W.M.; Girdauskas, E.; Delgado, V.; Abbara, S.; Lansac, E.; Prakash, S.K.; Bissell, M.M.; Popescu, B.A.; Hope, M.D.; Sitges, M.; Thourani, V.H.; Pibarot, P.; Chandrasekaran, K.; Lancellotti, P.; Borger, M.A.; Forrest, J.K.; Webb, J.; Milewicz, D.M.; Makkar, R.; Leon, M.B.; Sanders, S.P.; Markl, M.; Ferrari, V.A.; Roberts, W.C.; Song, J.K.; Blanke, P.; White, C.S.; Siu, S.; Svensson, L.G.; Braverman, A.C.; Bavaria, J.; Sundt, T.M.; Khoury, G. el; Paulis, R. de; Enriquez-Sarano, M.; Bax, J.J.; Otto, C.M.; Schafers, H.J.; Endorsed Heart Valve Soc HVS; European Assoc Cardiovasc Imaging; Soc Thoracic Surg STS; Amer Assoc Thoracic Surg AATS; Soc Cardiovasc Magnetic Resonance; Soc Cardiovasc Computed Tomography; North Amer Soc Cardiovasc Imaging; Int Bicuspid Aortic Valve Consorti
• Date: 2021-09-01
• Journal: European Journal of Cardio-Thoracic Surgery
• Volume: 60
• Issue: 3
• Pages: 448 - 476
• DOI: doi:10.1093/ejcts/ezab038
• Link: https://academic.oup.com/ejcts/article-pdf/60/3/448/40350560/ezab038.pdf