Rupture of a median sacral artery aneurysm in a patient with vascular Ehlers-Danlos syndrome

Abstract

Introduction: Vascular Ehlers Danlos syndrome is a rare connective tissue disease that is associated with various arterial complications.Report: A 25 year old man with vascular Ehlers Danlos syndrome presented with acute lower back pain as a result of a ruptured aneurysm of the median sacral artery (MSA). Prior medical history included several vascular events resulting in a right iliac occlusion. The unusual location of aneurysmal disease of the MSA might be explained by extensive collateral flow recruitment due to this occlusion.Conclusion: Previous vascular events inducing collateral recruitment might justify a more frequent follow up in patients with connective tissue disorders. (C) 2020 The Authors. Published by Elsevier Ltd on behalf of European Society for Vascular Surgery.

AneurysmConnective tissue diseaseMedian sacral arteryVascular Ehlers Danlos syndrome