International Consensus Statement on Nomenclature and Classification of the Congenital Bicuspid Aortic Valve and Its Aortopathy, for Clinical, Surgical, Interventional and Research Purposes

Author(s):
Michelena, H.I.; Corte, A. della; Evangelista, A.; Maleszewski, J.J.; Edwards, W.D.; Roman, M.J.; Devereux, R.B.; Fernandez, B.; Asch, F.M.; Barker, A.J.; Sierra-Galan, L.M.; Kerchove, L. de; Fernandes, S.M.; Fedak, P.W.M.; Girdauskas, E.; Delgado, V.; Abbara, S.; Lansac, E.; Prakash, S.K.; Bissell, M.M.; Popescu, B.A.; Hope, M.D.; Sitges, M.; Thourani, V.H.; Pibarot, P.; Chandrasekaran, K.; Lancellotti, P.; Borger, M.A.; Forrest, J.K.; Webb, J.; Milewicz, D.M.; Makkar, R.; Leon, M.B.; Sanders, S.P.; Markl, M.; Ferrari, V.A.; Roberts, W.C.; Song, J.K.; Blanke, P.; White, C.S.; Siu, S.; Svensson, L.G.; Braverman, A.C.; Bavaria, J.; Sundt, T.M.; Khoury, G. el; Paulis, R. de; Enriquez-Sarano, M.; Bax, J.J.; Otto, C.M.; Schafers, H.J.
Published
2021
Publication type
Article / Letter to editor

Abstract

This International Consensus Classification and Nomenclature for the congenital bicuspid aortic valve condition recognizes 3 types of bicuspid valves: 1. The fused type (right-left cusp fusion, right-non-coronary cusp fusion and left-non coronary cusp fusion phenotypes); 2. The 2-sinus type (latero-lateral and antero-posterior phenotypes); and 3. The partial-fusion (forme fruste) type. The presence of raphe and the symmetry of the fused type phenotypes are critical aspects to describe. The International Consensus also recognizes 3 types of bicuspid valve-associated aortopathy: 1. The ascending phenotype; 2. The root phenotype; and 3. Extended phenotypes. (Ann Thorac Surg 2021;112:e203-35) 2021 Jointly between The Society of Thoracic Surgeons, the American Association for Thoracic Surgery, the European Association for Cardio-Thoracic Surgery, and the Radiological Society of North America. Published by Elsevier Inc.

Date issued
2021-09-01
Language
English
Publisher
ELSEVIER SCIENCE INC
Is part of
Annals of Thoracic Surgery (2021), Vol. 112, no. 3, p. E203-E235
hdl
1887/3279709
doi
10.1016/j.athoracsur.2020.08.119